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THE CASE OF IDIOPATHIC PLEUROPARENCHYMAL FIBROELASTOSIS DIAGNOSED BY TRANSBRONCHIAL BIOPSY

HUSEYİN ARPAG, MUHAMMET SAYAN, NURHAN ATİLLA, FULSEN BOZKUS, HASAN KAHRAMAN, ABDULKADİR YASİR BAHAR, MAHMUT TOKUR

Eurasian Journal of Pulmonology - 2018;20(2):104-106

Departments of Chest Diseases, Thoracic Surgery and Pathology, Faculty of Medicine, Kahramanmaras Sutcu Imam University, Kahramanmaras, Turkey

 

Pleuroparenchymal fibroelastosis (PPFE) is claasified in idiopathic interstitial pneumonitis group is rarely seen. Etiology and pathophysiology of this entity are not completely understood. The prognosis is poor, and there is no effective treatment except for lung transplantation. Here, we presented a case of PPFE diagnosed by transbronchial biopsy through fiberoptic bronchoscopy and its histopathological and clinicoradiological features.