HUSEYİN ARPAG, MUHAMMET SAYAN, NURHAN ATİLLA, FULSEN BOZKUS, HASAN KAHRAMAN, ABDULKADİR YASİR BAHAR, MAHMUT TOKUR
Eurasian Journal of Pulmonology - 2018;20(2):104-106
Pleuroparenchymal fibroelastosis (PPFE) is claasified in idiopathic interstitial pneumonitis group is rarely seen. Etiology and pathophysiology of this entity are not completely understood. The prognosis is poor, and there is no effective treatment except for lung transplantation. Here, we presented a case of PPFE diagnosed by transbronchial biopsy through fiberoptic bronchoscopy and its histopathological and clinicoradiological features.