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CLASS I PENTALOGY OF CANTRELL: A RARE CASE REPORT

BAYRAM ALİ DORUM, HİLAL OZKAN, NİLGUN KOKSAL, YASEMİN DENKBOY ONGEN

The European Research Journal - 2017;3(1):83-86

Division of Neonatology, Department of Pediatrics, Uludag University School of Medicine, Bursa, Turkey

 

Pentalogy of Cantrell is characterized by the presence of five major congenital defects involving the abdominal wall, pericardium, diaphragm, lower sternum and various cardiac abnormalities. This rare syndrome was described by Cantrell in 1958 and it has poor prognosis. We report here a case of class I Cantrell syndrome and our aim is to share difficulties experienced and review the related literature.